|
Disclaimer:
Whonamedit.com does not give medical advice.
This survey of medical eponyms and the persons behind them is meant as a general interest site only. No information found here must under any circumstances be used for medical purposes, diagnostically, therapeutically or otherwise. If you, or anybody close to you, is affected, or believe to be affected, by any condition mentioned here: see a doctor.
|
A recommendation:
Hypography is an open community about science and all things related
|
|
|
Gsell-Erdheim syndrome
Also known as:
Erdheim’s cystic necrosis of aorta
Erdheim's disease
Associated persons:
Jakob Erdheim
Otto Gsell
Description:
A historic term for idiopathic necrosis of the medial layer of the aorta with subsequent formation of cysts, without inflammatory changes, often leading to aortic rupture. Assumed to be a frequent cause of aneurisma dissecans aorta - aorta dissection, a dramatic sequence of aortic rupture. Inheritance is autosomal dominant.
The first clinical observations and diagnosing was done already in 1856 by Swaine and Lathan. The first comprehensive in-depth clinical description of the disease picture was made by Gsell in 1928, while Erdheim in 1929 worked over the pathological anatomy and coined the term «medionecrosis aortae idiopathica».
Bibliography:
- O. Gsell:
Wandnekrosen der Aorta als selbständige Erkrankung und ihre Beziehung zur Spontanruptur. [Virchow’s] Archiv für pathologische Anatomie und Physiologie und für klinische Medizin, 1928, 270: 1-36.
- J. Erdheim:
Medionecrosis aortae idiopathica (cystica). [Virchow’s] Archiv für pathologische Anatomie und Physiologie und für klinische Medizin, 1929, 273: 454-479.
Medionecrosis aortae idiopathica cystica. [Virchow’s] Archiv für pathologische Anatomie und Physiologie und für klinische Medizin, 1930, 276: 187-229.
|
|
|
