Hamman-Rich syndrome

Alternative eponyms

Related people

Previously used term for acute diffuse idiopathic interstitial pulmonary fibrosis of unknown aetiology.

Description

Previously used term for acute diffuse idiopathic interstitial pulmonary fibrosis of unknown aetiology. Insidious onset followed by respiratory embarrassment, fatigability, loss of weight, cyanosis, right-sided heart failure and other abnormalities. It is usually fatal. Both sexes affected; slight male predominance; onset over broad age range, but highest incidence between 40 and 70 years of age. Aetiology unknown. Familial, autosomal dominant inheritance.

First described by Sir Dominic John Corrigan (1802-1880) in 1838, in 1897 by Georg Eduard Rindfleisch (1836-1908) as «cirrhosis cystica» and in 1915 by David Paul von Hansemann (1858-1920) as «lymphangitis reticularis».

Bibliography

  • D. J. Corrigan:
    On cirrhosis of the lung.
    The Dublin Journal of Medical Science, 1838, 13: 266-286.
  • G. E. Rindfleisch:
    Ueber Cirrhosis Cystica Pulmonum. Zentralblatt für allgemeine Pathologie und pathologische Anatomie, Jena, 1897, 8: 864–865.
  • L. Hamman, A. R. Rich:
    A clinical-pathological conference. A case of heart failure.
    International Clinics, 43d series, 1933: 1: 197-232
  • L. Hamman, A. R. Rich:
    Fulminant diffuse interstitial fibrosis of the lungs. Transactions of the American Clinical and Climatological Association, 1935, 51: 154-163.
  • L. Hamman, A. R. Rich:
    Acute diffuse interstitial fibrosis of the lungs.
    Bulletin of the Johns Hopkins Hospital, Baltimore, 1944, 74: 177-212.
  • S. Javaheri, D. H. Lederer, J.A. Pella, G. J. Mark and B.W. Levine:
    Idiopathic pulmonary fibrosis in monozygotic twins: the importance of genetic predisposition. Chest, 1980, 78: 591-594.
We thank Jim Loyd for information submitted.

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