Ramsay Hunt's paralysis
A disturbance with symptoms resembling those of the adult form of parkinsonism, but less intense than in Parkinson’s disease. It is characterised by tremor, bradykinesia, dysarthria, rigidity, fixed facies and a tendency to faint. Mental functions are intact and there are no reflex changes. It belongs to the groups of extrapyramidal disturbances and is caused by degeneration of the globus pallidus. Both sexes affected, onset between the ages of 10 and 30 years. Inheritance is autosomal dominant.
- H. Willige:
Über Paralysis agitans im Jugendlichen.
Zeitschrift für die Gesamte Neurologie und Psychiatrie, Berlin, 1911, 4: 520.
- J. R. Hunt:
Progressive atrophy of the globus pallidus (primary atrophy of the pallidal system). A system disease of the paralysis agitans type, characterized by atrophy of the motor cells of the corpus striatum. A contribution to the function of the corpus striatum.
Brain, Oxford, 1917; 40: 58-148.