|
Disclaimer:
Whonamedit.com does not give medical advice.
This survey of medical eponyms and the persons behind them is meant as a general interest site only. No information found here must under any circumstances be used for medical purposes, diagnostically, therapeutically or otherwise. If you, or anybody close to you, is affected, or believe to be affected, by any condition mentioned here: see a doctor.
|
A recommendation:
Hypography is an open community about science and all things related
|
|
|
Biber-Haab-Dimmer degeneration
Also known as:
Bücklers' syndrome II
Haab's degeneration
Haab’s syndrome
Haab-Dimmer syndrome
Reis-Bücklers syndrome
Associated persons:
Hugo Biber
Friedrich Dimmer
Otto Haab
Description:
A localised form of amyloidosis with onset early in life (20-30 years of age), affecting both sexes. It is manifested by progressive corneal opacity with distinct borders and a network of lattice-like branching filaments. Round spots may be scattered throughout the cornea, but the intervening spaces are clear, and there may be extracellular deposits of amyloid material. Visual function usually remains fairly satisfactory for long time. Aetiology unknown. Inheritance is autosomal dominant.
The terms Bücklers' syndrome II and Reis-Bücklers syndrome are misnomers. Reis-Bücklers syndrome is an annular corneal dystrophy. See under Heinrich Maria Wilhelm Reis, German ophthalmologist, born 1872.
Bibliography:
- H. Biber:
Über einige seltenere Hornhauterkrankungen. Zürich, 1890.
Inaugural Dissertation, Zurich, 1890. Cited by O. Haab: Die gittrige Keratitis.
- O. Haab:
Die gittrige Keratitis.
Zeitschrift für Augenheilkunde, Basel, 1899, 2: 235-246.
- F. Dimmer:
Über oberflächliche gittrige Hornhauttrübung.
Zeitschrift für Augenheilkunde, Basel, 1899, 2: 354.
- S. J. Kimura,M. C. Wayne:
Retinal Diseases. Philadelphia, Lea & Febiger, 1966.
|
|
|
