|
Disclaimer:
Whonamedit.com does not give medical advice.
This survey of medical eponyms and the persons behind them is meant as a general interest site only. No information found here must under any circumstances be used for medical purposes, diagnostically, therapeutically or otherwise. If you, or anybody close to you, is affected, or believe to be affected, by any condition mentioned here: see a doctor.
|
A recommendation:
Hypography is an open community about science and all things related
|
|
|
Debré-Lamy-Lyell syndrome
Also known as:
Fuchs-Salzmann-Terrier syndrome
Lyell's syndrome
Brocq-Debré-Lyell syndrome
Associated persons:
Louis-Anne-Jean Brocq
Robert Debré
Ernst Fuchs
Maurice Emile Joseph Lamy
Alan Lyell
Maximilian Salzmann
Description:
A rare syndrome characterized by a severe bullous eruption of the skin and mucous membranes, fever, malaise, conjunctivitis, and a diffuse erythema. Recovery is slow and contractures may form in the skin and mucous membranes. It may be a severe form of erythema multiforma and is frequently lethal in children and old people.
Aetiological factors are allergic reactions to a number of factors, e.g., sepsis, lymphoma, graft-versus-host disease, a variaty of drugs, most notably sulfonamides. Some drugs, bacterial (sometimes secondary to staphylococcal infection), viral and fungal infections, malignant disease especially lymphoma, vaccination and radiation.
Bibliography:
- E. Fuchs:
Über knochenförmige Hornhauttrübung.
Albrecht von Græfes Archiv für Ophthalmologie, 1902, 53: 423-435.
Über knochenförmige Hornhauttrübungen.
Albrecht von Græfes Archiv für Ophthalmologie, 1915, 89: 337-349.
- A. J. Brocq:
Schème des eruptions bulleuses. Le pemphigus subaigu malin à bulles extensives et faits connexes.
Annales de dermatologie et de syphilographie, Paris, 1919, 7: 449-461.
- R. Debré, M. Lamy, M. Lamotte:
Un cas d'erythrodermie avec épidermolyse chez un enfant de 12 ans.
Bulletins de la Société de Pédiatrie, 1939, 37: 231-238.
- A Lyell:
Toxic epidermal necrolysis: eruption resembling scalding of the skin.
The British Journal of Dermatology, Oxford, 1956, 68: 355-361.
|
|
|
