|
Disclaimer:
Whonamedit.com does not give medical advice.
This survey of medical eponyms and the persons behind them is meant as a general interest site only. No information found here must under any circumstances be used for medical purposes, diagnostically, therapeutically or otherwise. If you, or anybody close to you, is affected, or believe to be affected, by any condition mentioned here: see a doctor.
|
A recommendation:
Hypography is an open community about science and all things related
|
|
|
Bamberger-Marie disease
Also known as:
Bamberger-Pierre Marie syndrome
Bamberger's disease
Hagner's syndrome
Mankowsky’s disease (misnomer)
Pierre Marie's syndrome
Marie-Bamberger disease
von Bamberger’s disease
Associated persons:
Eugen von Bamberger
Nikolaus Friedreich
Karl and Wilhelm Hagner
Boris Nikitich Mankowsky
Pierre Marie
Description:
A syndrome characterised by clubbing of the fingers (Hippocratic fingers) and toes, periosteal new bone growth mainly in the long bones of the extremities, frequent evidence of joint involvement, and marked vasomotor disturbances involving hands and feet. It occurs in association with pulmonary disease such as bronchogenic carcinoma, occasional bronchiectasia, or lung abscesses. The syndrome is more common before middle life, and occurs more frequently in males.
Already 2300 years before Bamberger and Marie accounted for their findings Hippocrates in his book of prognoses had established that drumstick-fingers were a sign of severe disease in the lungs. The syndrome was first described by Nikolaus Friedreich in brothers Karl and Wilhelm Hagner, hence the synonym Hagner syndrome. A familial form of this syndrome is known as Mankowsky's syndrome.
Von Bamberger in 1889 described the condition in detail and pointed out the relationship of such clubbing to diseases of the heart and lungs. Marie in 1890 differentiated the syndrome from acromegaly.
Bibliography:
- N. Friedreich:
Hyperostose des gesamten Skeletts.
[Virchows] Archiv für pathologische Anatomie und Physiologie und für klinische Medicin, Berlin, 1868, 16: 83-87.
- E. von Bamberger:
Veränderungen der Röhrenknochen bei Bronchiektasie.
Wiener klinische Wochenschrift, 1889, 2: 226.
Über Knochenveränderungen bei chronischen Lungen- und Herzkrankheiten.
Zeitschrift für Klinische Medicin, Berlin, 1891, 18: 193-217.
- P. Marie:
De l’osteo-arthropathie hypertrophiante pneumique.
Rév Med, Paris, 1890, 10: 1-36.
- H. Kuhlewein:
Hyppocratis opera quae feruntur omnia. Leipzig, 1894-1902.
|
|
|
