Groenouw's syndrome II
Alternative eponyms
- Fehr's dystrophy
- Fehr's syndrome
- Groenouw's dystrophy II
- Bücklers' cornea dystrophy
Related people
Hereditary corneal dystrophy with onset in childhood, usually between 5 and 9 years, affecting both sexes.
Description
Hereditary corneal dystrophy with onset in childhood, usually between 5 and 9 years, affecting both sexes. Characterised by the appearance of discrete grey opacities scattered over the corneal surface, with intervening cloudy spaces. Significant reduction of vision by the age 30 to 40, when larger spots of various shapes become evident. Patients may be blind at age 40, occasionally later. Inherited as an autosomal recessive trait,
Bibliography
- A. Groenouw:
Knötchenförmige Hornhauttrübungen (Noduli corneae).
Archiv für Augenheilkunde, München, 1890, 21: 281-289. - O. Fehr:
Über familiäre, fleckige Hornhautentartung.
Zentralblatt für praktische Augenheilkunde, 1904, 28: 1-11.